An adult with pulmonary hipoplasia
Keywords:
LUNG/abnormalities, RESPIRATORY SYSTEM ABNORMALITIESAbstract
Pulmonary hypoplasia is an uncommon bronchopulmonary disease that is diagnosed during childhood. Patients with this condition usually present with a wide variety of symptoms, ranging from frequent respiratory infections to pain and respiratory dyspnea. Its causes are related to the invasion of the intrathoracic cavity or to anomalies of the urinary tract. This study presents the case of an adult patient with a past medical history of arterial hypertension and bronchial asthma, as well as repeated bronchitis until the age of 3 years and several pneumonias. He presents to the doctor’s office complaining of dyspnea. On auscultation an abolition of the vesicular breath sound at the base of the right lung is found. Investigations are ordered including chest X-ray, bronchoscopy and CT scan, which confirmed a diagnosis of pulmonary hypoplasia.Downloads
References
Acosta López J, Arrué Guerrero A, Torres Cuevas B L, Hierro García D, Tamayo M, Feliciano Álvarez V. Hemitórax opaco. Rev Cub Med Mil [revista en internet]. 2014, Mar [citado 12 de junio 2017]; 43(1). Disponible en: http://scieloprueba.sld.cu/scielo.php?script=sci_arttext&pid=S0138-65572014000100014 &lng=es.
Yamamoto Y, Hirose A, Jain V, Savard W, Hornberger L. EP08. 06: Prediction of severity of lung hypoplasia in the fetuses with prolonged premature rupture of membrane. Ultrasound in Obstetrics & Gynecology [revistas en internet]. 2016 [citado 12 de junio 2017]; 48(S1). Disponible en: http://onlinelibrary.wiley.com /doi/10.1002/uog.16886/full.
Mirchandani L V, Alam A, Iyer A, Kutty J T. Rare Case of Unilateral Hypoplasia of Lung with Associated Ventricular Mass in an Adult. Journal of Clinical and Diagnostic Research: JCDR [revista en internet]. 2016 [citado 12 de junio 2017]; 10(7). Disponible en: https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5020255/.
Umeda S, Miyagawa S, Fukushima S, Oda N, Saito A, Sakai, Y, et al. Enhanced Pulmonary Vascular and Alveolar Development via Prenatal Administration of a Slow-Release Synthetic Prostacyclin Agonist in Rat Fetal Lung Hypoplasia. PloS one [revista en internet]. 2016 [citado 12 de junio 2017]; 11(8). Disponible en: http://journals.plos.org/plosone/article?id=10.1371/journal.pone.0161334.
Sugiura Y, Fujimoto H, Naruke M, Hashizume T, Kaseda S, Nemoto E. The first rib hypoplasia and the aberrant pulmonary artery branch detected by three-dimensional computed tomography in a surgical case with apical lung cancer, a case report. BMC Surgery [revista en internet]. 2017 [citado 12 de junio 2017]; 17(1). Disponble en: https://bmcsurg.biomedcentral.com/articles/10.1186/s12893-016-0199-1.
Wert S E, Wikenheiser-Brokamp K A. Congenital Malformations of the Lung. Fetal & Neonatal Lung Development [revista en internet]. 2016 [citado 12 de junio 2017]; 94. Disponible en: https://books.google.com.cu/books?hl=es&lr=&id=YPjUCwAAQBAJ&oi=fnd&pg=PA94&dq=unilateral+ lung+hypopl.
He H, Sun F, Ren W, Wang Y, Xu S. Diagnostic value of echocardiography in isolated congenital unilateral lung agenesis combined with different anomalies: Two rare cases in children. Journal of Clinical Ultrasound [revista en internet]. 2016 [citado 12 de junio 2017]; 44(8). Disponible en: http://onlinelibrary.wiley.com/doi/10.1002/jcu.22340/pdf.
Roy PP, Datta S, Sarkar A, Das A, Das S. Unilateral pulmonary agenesis presenting in adulthood. Respiratory Medicine Case Reports [revista en internet]. 2012 [citado 12 de junio 2017]; 5. Disponible en: http://www.sciencedirect.com/science/article/pii/S1755001711000431.
Komolafe F, Dahniya M H, Al-Ali Y, Al-Zaabi L, Aziz F. Asymptomatic unilateral pulmonary hypoplasia/agenesis in adults: A report of six cases. West African Journal of Radiology [revista en internet]. 2017 [citado 12 de junio 2017]; 24(1). Disponible en: http://www.wajradiology.org/article.asp?issn=1115-3474;year= 2017;volume=24;issue=1;spage=99;epage=103;aulast=Komolafe.
Eltayeb O, Mongé M C, Popescu A R, Sarwark A E, Harris T, Backer C L. Discontinuous Pulmonary Artery Utility of Computed Tomographic Angiography and Lung Perfusion Scan in Management. World Journal for Pediatric and Congenital Heart Surgery [revista en internet]. 2017 [citado 12 de junio 2017]; 8(1): 106-110. Disponible en: http://journals.sagepub.com/doi/abs/10.1177/2150135115618871.
Devi YG, Rani NU, Rao GS, Narayana M, Kumar BD. A rare clinical presentation of primary pulmonary hypoplasia with tuberculous pleural effusion. IJSS Case Reports & Reviews [revista en internet]. 2014 [citado 12 de junio 2017]; 1(3). Disponible en: http://imsear.li.mahidol.ac.th/handle/123456789/159315.
Upadhyay H, Contreras J, Hashemi Z, Khokar A, Nangrani K, Arjomand F, et al. Dyspnoea in a patient with unilateral lung agenesis. Postgraduate medical journal [revista en internet]. 2016 [citado 12 de junio 2017]; 92(1094). Disponible en: http://pmj.bmj.com/content/92/1094/744.
Downloads
Published
How to Cite
Issue
Section
License
This journal provides free and immediate access to its content under the principle that making research freely available to the public supports a greater exchange of global knowledge. This means that the authors transfer the copyright to the journal, so that copies and distribution of the contents can be made by any means, as long as the authors' acknowledgment is maintained. These terms are a reflection that the journal assumes copyright under Creative Commons licenses, specifically under a Creative Commons Attribution 4.0 International license.
Registration and submission of articles to the journal is free. The processing, including review, editing and publication, is completely free of charge.